Search on: AMINOLEVULINIC ACID DEHYDRATASE 
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Descriptor English:   Porphobilinogen Synthase 
Descriptor Spanish:   Porfobilinógeno Sintasa 
Descriptor Portuguese:   Sintase do Porfobilinogênio 
Synonyms English:   Aminolevulinate Hydro-Lyase
Aminolevulinic Acid Dehydratase  
Tree Number:   D08.811.520.241.300.550
Definition English:   An enzyme that catalyzes the formation of porphobilinogen from two molecules of 5-aminolevulinic acid. EC 4.2.1.24. 
Indexing Annotation English:   DF: ALA DEHYDRASE
History Note English:   98(73) 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DF deficiency
DU diagnostic use DE drug effects
EC economics GE genetics
HI history IM immunology
IP isolation & purification ME metabolism
PK pharmacokinetics PD pharmacology
PH physiology PO poisoning
RE radiation effects SE secretion
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UL ultrastructure UR urine
Record Number:   633 
Unique Identifier:   D000623 

Occurrence in VHL:
 

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