Search on: ASPARTYLGLUCOSYLAMINE DEASPARTYLASE 
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Descriptor English:   Aspartylglucosylaminase 
Descriptor Spanish:   Aspartilglucosilaminasa 
Descriptor Portuguese:   Aspartilglucosilaminase 
Synonyms English:   Aspartylglucosaminidase
Aspartylglucosylamine Deaspartylase
Aspartylglycosamine Amidohydrolase  
Tree Number:   D08.811.277.087.125
Definition English:   An enzyme that catalyzes the conversion of N(4)-(beta-N-acetyl-D-glucosaminyl)-L-asparagine and water to N-acetyl-beta-D-glucosaminylamine and L-aspartate. It acts only on asparagine-oligosaccharides containing one amino acid, i.e. the ASPARAGINE has free alpha-amino and alpha-carboxyl groups. (From Enzyme Nomenclature, 1992) 
Entry Combination - descr/qualif English:   Aspartylglucosylaminase/deficiency use Aspartylglucosaminuria
 
History Note English:   91(75); was see under AMIDOHYDROLASES 1975-90 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DU diagnostic use
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
SE secretion ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Record Number:   1234 
Unique Identifier:   D001227 

Occurrence in VHL:
 

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