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BULBAR PALSY, PROGRESSIVE
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DeCS
Descriptor
English
:
Bulbar Palsy, Progressive
Descriptor
Spanish
:
Parálisis Bulbar Progresiva
Descriptor
Portuguese
:
Paralisia Bulbar Progressiva
Synonyms
English
:
Paralysis, Bulbar
Fazio-Londe Syndrome
Tree Number:
C10.574.562.300
C10.668.467.300
Definition
English
:
A
motor neuron disease
marked by progressive weakness of the
muscles
innervated by
cranial nerves
of the lower
brain stem
. Clinical manifestations include
dysarthria
, dysphagia, facial weakness,
tongue
weakness, and fasciculations of the
tongue
and
facial muscles
. The
adult
form of the
disease
is marked initially by bulbar weakness which progresses to involve
motor neurons
throughout the neuroaxis. Eventually this condition may become indistinguishable from
AMYOTROPHIC LATERAL SCLEROSIS
. Fazio-Londe
syndrome
is an inherited form of this illness which occurs in children and young adults. (Adams et al., Principles of
Neurology
, 6th ed, p1091;
Brain
1992 Dec;115(Pt 6):1889-1900)
History Note
English
:
2000(1966)
Allowable Qualifiers
English
:
BL
blood
CF
cerebrospinal fluid
CI
chemically induced
CL
classification
CO
complications
CN
congenital
DI
diagnosis
DH
diet therapy
DT
drug therapy
EC
economics
EM
embryology
EN
enzymology
EP
epidemiology
EH
ethnology
ET
etiology
GE
genetics
HI
history
IM
immunology
ME
metabolism
MI
microbiology
MO
mortality
NU
nursing
PS
parasitology
PA
pathology
PP
physiopathology
PC
prevention & control
PX
psychology
RA
radiography
RI
radionuclide imaging
RT
radiotherapy
RH
rehabilitation
SU
surgery
TH
therapy
US
ultrasonography
UR
urine
VE
veterinary
VI
virology
Record Number:
10433
Unique Identifier:
D010244
Occurrence in VHL
:
Similar:
DeCS
CID-10
SciELO
LILACS
LIS