Search on: CYSTATHIONINE GAMMA-LYASE 
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Descriptor English:   Cystathionine gamma-Lyase 
Descriptor Spanish:   Cistationina gammaliasa 
Descriptor Portuguese:   Cistationina gama-Liase 
Synonyms English:   Cystathionase
Cysteine Desulfhydrase
Cystine Desulfhydrase
gamma-Cystathionase
Homoserine Deaminase
Homoserine Dehydratase  
Tree Number:   D08.811.520.300.250
Definition English:   A multifunctional pyridoxal phosphate enzyme. In the final step in the biosynthesis of cysteine it catalyzes the cleavage of cystathionine to yield cysteine, ammonia, and 2-ketobutyrate. EC 4.4.1.1. 
Indexing Annotation English:   /defic: consider also CYSTATHIONINE /urine (IM) + AMINO ACID METABOLISM, INBORN ERRORS (IM)
History Note English:   91(75); was see under LYASES 1975-90 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DF deficiency
DU diagnostic use DE drug effects
EC economics GE genetics
HI history IM immunology
IP isolation & purification ME metabolism
PK pharmacokinetics PD pharmacology
PH physiology PO poisoning
RE radiation effects SE secretion
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UL ultrastructure UR urine
Record Number:   3561 
Unique Identifier:   D003542 

Occurrence in VHL:
 

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