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HEMOGLOBINURIA, PAROXYSMAL
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DeCS
Descriptor
English
:
Hemoglobinuria, Paroxysmal
Descriptor
Spanish
:
Hemoglobinuria Paroxística
Descriptor
Portuguese
:
Hemoglobinúria Paroxística
Synonyms
English
:
Paroxysmal Cold Hemoglobinuria
Paroxysmal Nocturnal Hemoglobinuria
Tree Number:
C15.378.071.141.560
C15.378.190.625.460
Definition
English
:
A condition characterized by the
recurrence
of
HEMOGLOBINURIA
caused by intravascular
HEMOLYSIS
. In cases occurring upon cold exposure (paroxysmal cold
hemoglobinuria
), usually after infections, there is a circulating antibody which is also a cold hemolysin. In cases occurring during or after
sleep
(paroxysmal nocturnal
hemoglobinuria
), the clonal
hematopoietic stem cells
exhibit a global deficiency of
cell membrane
proteins.
History Note
English
:
78; was MARCHIAFAVA-MICHELI SYNDROME 1963-77
Allowable Qualifiers
English
:
BL
blood
CF
cerebrospinal fluid
CI
chemically induced
CL
classification
CO
complications
CN
congenital
DI
diagnosis
DH
diet therapy
DT
drug therapy
EC
economics
EM
embryology
EN
enzymology
EP
epidemiology
EH
ethnology
ET
etiology
GE
genetics
HI
history
IM
immunology
ME
metabolism
MI
microbiology
MO
mortality
NU
nursing
PS
parasitology
PA
pathology
PP
physiopathology
PC
prevention & control
PX
psychology
RA
radiography
RI
radionuclide imaging
RT
radiotherapy
RH
rehabilitation
SU
surgery
TH
therapy
US
ultrasonography
UR
urine
VE
veterinary
VI
virology
Record Number:
6607
Unique Identifier:
D006457
Occurrence in VHL
:
Similar:
DeCS
CID-10
SciELO
LILACS
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